| 产品详情 |
| Edit |   |
|---|
| Product Name | ACADSB, Recombinant, Human, aa34-432, His-tag |
|---|
| Description | Purity ~90% (SDS-PAGE). Short/branched chain specific acyl-CoA dehydrogenase(ACADSB), is a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. ACADSB catalyzes the degradation of L-isoleucine and has the highest affinity for (s)-2-methylbutyryl-CoA, isobutyryl-CoA and 2-methylhexanoyl-CoA as substrates. Defects in ACADSB are the cause of short/branched-chain acyl-CoA dehydrogenase deficiency (SBCADD), an autosomal recessive disorder characterized by an increase of 2-methylbutyrylglycine and 2-methylbutyrylcarnitine in blood and urine. Source: Recombinant protein corresponding to aa34-432 from human ACADSB, fused to His-tag at N-terminal expressed in E. coli. Molecular Weight: ~46.4kD (424aa) AA |
|---|
| Size | 50ug, 250ug |
|---|
| Concentration | n/a |
|---|
| Applications | n/a |
|---|
| Other Names | ACADSB, Recombinant, Human, aa34-432, His-Tag (Short/branched chain specific acyl-CoA Dehydrogenase, Mitochondrial, 2-MEBCAD, ACAD7, SBCAD) |
|---|
| Gene, Accession, CAS # | Accession: NP_001600 |
|---|
| Catalog # | 351044 |
|---|
| Price | |
|---|
| Order / More Info | ACADSB, Recombinant, Human, aa34-432, His-tag from UNITED STATES BIOLOGICAL |
|---|
| Product Specific References | n/a |
|---|
| 产品资料 |
|
|