产品名称 Recombinant Pig Medium-chain specific acyl-CoA dehydrogenase, mitochondrial (ACADM) from MYBIOSOURCE INC.
产品货号 MBS949717
产品价格 现货询价,电话:010-67529703
产品规格 0.05 mg (E-Coli), 0.05 mg (Baculovirus), 0.2 mg (E-Coli), 0.5 mg (E-Coli), 0.2 mg (Yeast)
产品品牌 MYBIOSOURCE INC.
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Product NameRecombinant Pig Medium-chain specific acyl-CoA dehydrogenase, mitochondrial (ACADM)
Description26-421aa, Full Length of Mature Protein. MW: 46,485 Da. Purity >85% (SDS-PAGE). This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternati
Size0.05 mg (E-Coli), 0.05 mg (Baculovirus), 0.2 mg (E-Coli), 0.5 mg (E-Coli), 0.2 mg (Yeast)
Concentrationn/a
Applicationsn/a
Other Names[medium-chain specific acyl-CoA dehydrogenase, mitochondrial; Medium-chain specific acyl-CoA dehydrogenase, mitochondrial; medium-chain specific acyl-CoA dehydrogenase, mitochondrial]
Gene, Accession, CAS #ACADM, Gene ID: 397104, Accession: NP_999204.1
Catalog #MBS949717
Price
Order / More InfoRecombinant Pig Medium-chain specific acyl-CoA dehydrogenase, mitochondrial (ACADM) from MYBIOSOURCE INC.
Product Specific Referencesn/a
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